Received: 31.10.2022; Accepted: 10.11.2022; Published on-line: 21.12.2022

A case of Susac’s syndrome: bilateral retinal vessel occlusion in the presence of autoimmune inflammatory endotheliopathy

N. A. Ulianova 1, O. V. Zborovska 1, O. D. Shulga 2, 3

1 SI «The Filatov Institute of Eye Diseases and Tissue Therapy of the NAMS of Ukraine»; Odesa (Ukraine)

2 Volyn Regional Clinical Hospital; Lutsk (Ukraine)

3 Lesya Ukrainka Volyn National University; Lutsk (Ukraine)

TO CITE THIS ARTICLE: Ulianova NA, Zborovska OV, Shulga  OD. A case of Susac’s syndrome: bilateral retinal vessel occlusion in the presence of autoimmune inflammatory endotheliopathy. J.ophthalmol.(Ukraine).2022;6:65-69.  http://doi.org/10.31288/oftalmolzh202266569    


The paper presents a case with a classic triad (bilateral inferotemporal branch retinal artery occlusion (BRAO), multifocal callosal micro-infarcts, and sensorineural hearing loss) of Susac’s syndrome in a female patient following COVID-19 infection. We report clinical examination data, particularly, eye examination data and neurological status with brain magnetic resonance imaging (MRI) results. Special attention was given to the diagnostic value of optical coherence tomography (OCT) in Susac’s syndrome, which allows detecting characteristic focal atrophic changes in the inner retina with a preserved structure of the photoreceptor layer. Identification of the typical neurological, ocular or otological symptoms should raise suspicion for the syndrome, which is critical for early administration of the systemic steroid therapy.

Keywords: Susac’s syndrome, autoimmune inflammatory endotheliopayhy, retinal artery occlusion



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Corresponding author: Ulianova N. A., e-mail: ulyanova@ukr.net

Author Contributions: Ulianova N.A.: Conceptualization, Writing – original draft, Determining the patient’s ophthalmological status; Zborovska O.V.: Conceptualization, Writing – original draft, Performing the Differential Diagnosis; Shulga O.D.: Writing – original draft, Determining the Patient’s Neurological Status, Magnet Resonance Imaging. All authors reviewed the results and approved the final version of the manuscript.

Disclaimer. The opinions presented in this article are those of the authors and do not necessarily represent those of their institutions.

Ethical statement. Informed consent was obtained from the participant of the study.

Financial support. No financial support was received for this work.

Conflict of Interest Statement. No author reports any relevant conflicts of interest.