Received: 19 February 2019; Published on-line: 27 June 2019


A Case Report of Kussmaul-Maier Disease

O.O. Andrushkova, Cand Sc (Med); N.V. Malachkova, Cand Sc (Med); K.Iu. Grizhimalskaia, Cand Sc (Med); Ie.G. Manko, Student; T.M. Zhmud, Cand Sc (Med)

Vinnitsa National Pirogov Memorial Medical University; 

Vinnitsa (Ukraine)

E-mail: gtatyana@email.ua

Background: Kussmaul-Maier disease (also known as polyarteritis nodosa or PAN) is a systemic disorder characterized by destructive and proliferative changes in the walls of arteries (mainly muscular arteries and arterioles).

Purpose: To present a case exemplifying the ocular manifestations of Kussmaul-Maier disease.

Materials and Methods: The patient underwent visual acuity assessment, tonometry, and comprehensive eye examination. In addition, she underwent brain MRI and duplex sonography of the major arteries supplying the head. 

Results and conclusion: This case demonstrates the features of disease course and ophthalmologist’s tactics in the treatment of Kussmaul-Maier disease. Kussmaul-Maier disease has a recurrent course with long-lasting (as long as 11 years) periods of remission and favorable visual prognosis.

Keywords: Kussmaul-Maier disease, periarteritis nodosa


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The authors certify that they have no conflicts of interest in the subject matter or materials discussed in this manuscript.